subject area of
- An engineered interdomain disulfide bond stabilizes human blood coagulation factor viiia Academic Article
- Cargo delivery kinetics of cell-penetrating peptides Academic Article
- Complex-formation between bovine neurophysin-I and oxytocin, vasopressin, and tripeptide analogs of their NH2-terminal region - absorbance and circular-dichroism difference spectroscopic studies Academic Article
- Cystinosin, the protein defective in cystinosis, is a h+-driven lysosomal cystine transporter Academic Article
- Expression and characterization of von Willebrand factor dimerization defects in different types of von Willebrand disease Academic Article
- Fluorescence-based measurement of cystine uptake through xCT shows requirement for ROS detoxification in activated lymphocytes Academic Article
- Glutathione precursors replenish decreased glutathione pool in cystinotic cell lines Academic Article
- Hematopoietic stem cell gene therapy for the multisystemic lysosomal storage disorder cystinosis Academic Article
- Impairment of chaperone-mediated autophagy leads to selective lysosomal degradation defects in the lysosomal storage disease cystinosis Academic Article
- Inflammasome activation by cystine crystals: implications for the pathogenesis of cystinosis Academic Article
- Intralysosomal cystine accumulation in mice lacking cystinosin, the protein defective in cystinosis Academic Article
- Isolation and characterization of a mitogen from pokeweed (phytolacca americana) Academic Article
- Isolation and chemical properties of porcine thyrocalcitonin Academic Article
- Mechanism of action of enzymes catalyzing thiol-disulfide interchange. Thioltransferases rather than transhydrogenases Academic Article
- Molecular pathogenesis of cystinosis: Effect of ctns mutations on the transport activity and subcellular localization of cystinosin Academic Article
- Molecularly defined antibody conjugation through a selenocysteine interface Academic Article
- Platelets with a W127X mutation in GPIX express sufficient residual amounts of GPIbα to support adhesion to von Willebrand factor and collagen Academic Article
- Probing the non-native H helix translocation in apomyoglobin folding intermediates Academic Article
- Quantitative in vivo and ex vivo confocal microscopy analysis of corneal cystine crystals in the Ctns(-/-) knockout mouse Academic Article
- Structural basis for substrate targeting and catalysis by fungal polysaccharide monooxygenases Academic Article
- Synthetic symmetrization in the crystallization and structure determination of CelA from Thermotoga maritima Academic Article
- Systemic depletion of L-cyst(e)ine with cyst(e)inase increases reactive oxygen species and suppresses tumor growth Academic Article
- The covalent structure of a human gamma g-immunoglobulin. 4. The interchain disulfide bonds Academic Article
- The covalent structure of a human gamma g-immunoglobulin. X. Intrachain disulfide bonds Academic Article
- The covalent structure of an entire gammag immunoglobulin molecule Academic Article
- Upregulation of the Rab27a-dependent trafficking and secretory mechanisms improves lysosomal transport, alleviates endoplasmic reticulum stress, and reduces lysosome overload in cystinosis Academic Article